Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy: Report of an autopsy case.
- Author:
Tae Yub KIM
;
Young Min KIM
;
Jae Gul CHUNG
;
Gyung Yub GONG
;
Su Kil PARK
;
In Chul LEE
;
Joo Ryung HUH
- Publication Type:Case Report
- Keywords:
Right ventricular dysplasia/cardiomyopathy;
Arrhythmogenic dysplasia;
Sudden death
- MeSH:
Adult;
Atrioventricular Block;
Autopsy*;
Bundle-Branch Block;
Death, Sudden;
Edema;
Electrocardiography;
Heart Ventricles;
Hospitalization;
Humans;
Hypotension;
Lower Extremity;
Muscle Weakness;
Myocardium;
Systolic Murmurs;
Tachycardia, Ventricular;
Young Adult
- From:Korean Journal of Pathology
1997;31(11):1233-1236
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
A 35-year-old man was admitted with a 20 day history of generalized edema and muscular weakness of the lower extremities. He was alert with a pale puffy face and an ejection murmur was heard at the cardiac apex. The electrocardiogram disclosed low voltage, first degree atrioventricular block, and a right bundle branch block. During the hospitalization an intractable diastolic hypotension developed, which measured 0 mmHg at the lowest point. At that time the echocardiogram revealed a dilated, akinetic right ventricle. Eventually a multiorgan failure developed and an autopsy following his death presented a fibrofatty replacement of the right ventricular myocardium. This might be a case of an arrhythmogenic right ventricular dysplasia/cardiomyopathy, which is usually characterized clinically by a ventricular tachycardia and may cause a sudden death in young adults.
