Two Cases of the Landau-Kleffner Syndrome.
- Author:
Hoon Young WOO
1
;
Sang Won CHUNG
;
Dong Hoon HAN
;
Chul Kyu CHO
Author Information
1. Department of Otolaryngology-Head & Neck Surgery, Sanggye Paik Hospital, College of Medicine, Inje University, Seoul, Korea. pk29597@freechal.com
- Publication Type:Case Report
- Keywords:
Landau-Kleffner syndrome;
Auditory agnosia;
Epilepsy
- MeSH:
Agnosia;
Audiometry;
Brain Stem;
Epilepsy;
Hearing;
Hearing Tests;
Landau-Kleffner Syndrome*
- From:Korean Journal of Otolaryngology - Head and Neck Surgery
2004;47(3):268-271
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Landau-Kleffner syndrome, or acquired epileptiform aphasia, is an epilepsy syndrome with variable disruption of acquired language and epileptiform discharges on electroencephalograph (EEG). Auditory agnosia can deteriorate into total unresponsiveness and impaired expressive communication. In spite of the presence of this condition, the pure tone audiometry, otoacoustic emission and brainstem evoked auditory potential could be normal. Therefore, in the above hearing tests which are the mainstream methods for pediatric hearing evaluation, otolaryngologists should have suspicion for the presence of this syndrome, although it is rare.
