A Case of an Adult-Onset Langerhans Cell Histiocytosis Involving the Temporal Bone.
10.3342/kjorl-hns.2013.56.7.465
- Author:
Kwang Joong KIM
1
;
Dae Keun LYM
;
Won Kyoung KONG
;
Seung Ho SHIN
Author Information
1. Department of Otorhinolaryngology-Head and Neck Surgery, CHA Bundang Medical Center, CHA University, Seongnam, Korea. drshinsh@gmail.com
- Publication Type:Case Report
- Keywords:
Adult;
External auditory canal;
Langerhans cell histiocytosis;
Temporal bone
- MeSH:
Adult;
Biopsy;
Ear Canal;
Histiocytosis, Langerhans-Cell;
Humans;
Langerhans Cells;
Rare Diseases;
Temporal Bone
- From:Korean Journal of Otolaryngology - Head and Neck Surgery
2013;56(7):465-468
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Langerhans cell histiocytosis (LCH) is a rare disease characterized by clonal proliferation of Langerhans cells. The temporal bone is frequently involved in pediatric LCH cases, but there have been few reports of adult LCH with temporal bone involvement. We present a case of adult onset LCH affecting the temporal bone. The diagnosis was made by biopsy, based on histopathologic findings of Langerhans cells. Diagnostic and therapeutic considerations of LCH involving the temporal bone are discussed.