A Case of the Audiotory Neuropathy.
- Author:
Hoon Young WOO
1
;
Moo Wan KANG
;
Jeong Hwan CHOI
;
Sang Won JUNG
Author Information
1. Department of Otorhinolaryngology, Inje University, College of Medicine, Seoul, Korea. hywoo@sanggyepaik.or.kr
- Publication Type:Case Report
- Keywords:
Auditory neuropathy;
Auditory brain stem evoked potential;
Otoacoustic emissisons
- MeSH:
Cochlear Nerve;
Discrimination (Psychology);
Ear, Inner;
Evoked Potentials, Auditory, Brain Stem;
Hair;
Hearing;
Hearing Disorders;
Hearing Loss;
Humans;
Peripheral Nervous System Diseases
- From:Korean Journal of Otolaryngology - Head and Neck Surgery
2001;44(9):982-985
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Auditory neuropathy is a recently described hearing disorder in which patients demonstrate hearing loss for pure tones, impaired word discrimination out of proportion to pure tone loss, absent or abnormal auditory brainstem responses (ABR), but normal outer hair cell function as measured by otoacoustic emissions and cochlear microphonics. Auditory neuropathy affects the normal synchronous activity in the auditory nerve, without affecting the amplification function in the inner ear. There is impairment in their temporal processing in the auditory nerve. So patients can hear sounds, but can not understand speech. Auditory neuropathy occurs either in isolation or as a part of a generalized neuropathy. We have identified one pediatric patient who demonstrated hearing defects and developed signs for peripheral neuropathy. We report it with a review of literatures.
