A Case of Cochlear Implantation in Neurofibromatosis Type II.
10.3342/kjorl-hns.2015.58.7.509
- Author:
Se Joon OH
1
;
Ji Hwan PARK
;
Keun Ik YI
;
Eui Kyung GOH
Author Information
1. Department of Otorhinolaryngology-Head and Neck Surgery, Pusan National University School of Medicine and Medical Research Institute, Busan, Korea. gohek@pusan.ac.kr
- Publication Type:Case Report
- Keywords:
Cochlear implantation;
Gamma Knife radiosurgery;
Neurofibromatosis 2
- MeSH:
Auditory Brain Stem Implantation;
Auditory Brain Stem Implants;
Cochlear Implantation*;
Cochlear Implants*;
Cochlear Nerve;
Hearing;
Hearing Loss;
Hearing Loss, Sensorineural;
Humans;
Neurofibromatosis 2*;
Neuroma, Acoustic;
Radiosurgery;
Rehabilitation;
Speech Perception
- From:Korean Journal of Otolaryngology - Head and Neck Surgery
2015;58(7):509-513
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Patients with neurofibromatosis type 2 (NF2) develop bilateral vestibular schwannomas that can cause binaural progressive hearing loss in most individuals. Auditory rehabilitation for bilateral profound sensorineural hearing loss in patients with NF2 poses a great therapeutic challenge. An auditory brainstem implantation may be an option after tumor excision, but its hearing results are still relatively unsatisfactory. A cochlear implantation (CI) may be another option in those cases where the cochlear nerve has been left intact after tumor excision or in those cases that have been kept stable after treating with Gamma-Knife. Here we report a case of undergoing CI after having been treated with Gamma-Knife in NF2 and showing improved open-set speech perception.
