A Case of Malignant Triton Tumor In Nasal Cavity.
- Author:
In Bong KANG
1
;
Seon Tae KIM
;
Seung Yeon HA
;
Geon CHOI
Author Information
1. Department of Otolaryngology-Head and Neck Surgery, Joong Ang Gil Hospital, Incheon, Korea.
- Publication Type:Case Report
- Keywords:
Malignant Triton tumor;
Nasal cavity
- MeSH:
Ethmoid Sinus;
Extremities;
Head;
Mitosis;
Nasal Cavity*;
Neck;
Necrosis;
Neoplasm Metastasis;
Neptune*;
Neurilemmoma;
Sarcoma
- From:Korean Journal of Otolaryngology - Head and Neck Surgery
1998;41(1):130-135
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Malignant triton tumor is a rare and usually aggressive sarcoma consisting of a malignant schwannoma with rhabdomyoblastic differentiation. Although this tumor is usually found at the extremities, 20% of cases are located in the head and neck region. This unusual tumor has not yet been described in the Korean Journal of Otolaryngology-Head and Neck Surgery. Malignant triton tumor is histologically high-grade, with large numbers of mitoses, prominent necrosis, and cellular pleomorphism. The clinical course for malignant triton tumor is usually one of rapid growth, early metastasis, and poor outcome in spite of therapy. Recently we experienced a case of malignant triton tumor, which involved the nasal cavity, maxillary and ethmoid sinus. The malignant tumor was treated with wide surgical excision followed by radiation therapy.
