Case Report of Mixed Connective Tissue Disease Complicating Pulmonary Hypertension and Its Literature Review
- VernacularTitle:混合性结缔组织病并肺动脉高压1例并文献复习
- Author:
zhi-hong, ZHUO
;
pei-chao, TIAN
;
huai-li, WANG
;
tie-zheng, GAO
- Publication Type:Journal Article
- Keywords:
mixed connective tissue disease;
pulmonary hypertension;
child
- From:Journal of Applied Clinical Pediatrics
2006;0(21):-
- CountryChina
- Language:Chinese
-
Abstract:
Objective To investigate the diagnosis and treatment of mixed connective tissue disease(MCTD)complicating pulmonary hypertension(PAH) in childhood in order to improve the recognition of this disease.Method According to the symptoms,signs,past history,labratory examinations,the child′s disease was diagnosed and treated,and the relative literature was reviewed.Results The main symptom of the child was interruptable apsychia.Ultrasound showed severe PAH,positive of anti-RNP antibody.After given immunosuppressant and decreased PAH,the patient′s condition was more improved.Conclusions MCTD complicating PAH in childhood onstes delitescently,and it′s difficult to diagnose.Recognition should be elevated to diagnose and treat it earlier.The prognosis can be improved.