A rare case of superficial polyfibromatosis in a Filipino male adolescent.
- Author:
Alvin Glen
;
Jamora Maria Jasmin J.
- Publication Type:Journal Article
- Keywords: Polyfibromatosis; Superficial Fibromatoses; Palmar Fibromatosis; Fibroblastic Rheumatism
- MeSH: Human; Male; Adolescent; Administration, Cutaneous; Fibroblasts; Hypertrophy; Nose; Range Of Motion, Articular; Skin; Skin Diseases; Stromal Cells; ; Dupuytren Contracture
- From: Journal of the Philippine Dermatological Society 2009;18(1):41-45
- CountryPhilippines
- Language:English
-
Abstract:
The superficial fibramatoses are a rare group of mainly benign disorders that clinically manifest as slow progressive dermal hypertrophies. This bewildering group of dermal matrix proliferation is composed of fibrous tissue, fibroblastic cells or spindle stromal cells with varying degrees of cellularity. Skin lesions are usually solitary or localized to a specific site of predilection. This is a case of a 15-year-old Filipino boy, presenting with asymptomatic firm, skin colored to erythematous papules and nodules on his limbs and nose. The lesions slowly worsened, resulting in flexion deformity and limited range of motion of both hands.