Bilateral microtia, canal atresia and aplasia of cochleovestibular nerve
- Author:
Asma binti Abdullah
;
Roslenda Abdul Rahman
;
Fadzilah Ismail
;
Mazita Ami
;
Marina Mat Baki
;
Aini Ab Aziz
- Publication Type:Case Reports
- Keywords:
Microtia;
canal atresia;
cochleovestibular nerve aplasia;
inner ear anomaly
- MeSH:
Congenital Microtia
- From:
The Medical Journal of Malaysia
2017;72(2):135-137
- CountryMalaysia
- Language:English
-
Abstract:
A six-month-old baby with congenital patent ductus
arteriosus (PDA), bilateral microtia and canal atresia was
referred for hearing assessment. The audiology assessment
revealed bilateral profound hearing loss, which is atypical
for a case of pure canal atresia. Imaging was performed
much earlier than usual and, as suspected, the patient also
had bilateral severe inner ear anomaly. It is extremely rare
for a person to have both external and inner ear anomaly
because of the different embryological origin. The only
suitable hearing rehabilitation option for this kind of patients
is brainstem implant. However, the parents had opted for
sign language as a form of communication.
KEY WORDS:
Microtia; canal atresia; cochleovestibular nerve aplasia; inner ear anomaly
- Full text:P020170509460014933011.pdf
