Bilateral pure gonadoblastoma in a 46 XY individual--a case report.
- Author:
M A Siti Aishah
;
R Chandran
;
H Tahir
- Publication Type:Journal Article
- MeSH:
Right and left;
Gonadoblastoma;
Gonads;
Female;
Case Report
- From:
The Medical journal of Malaysia
1991;46(4):384-7
- CountryMalaysia
- Language:Malay
-
Abstract:
We report here a rare case of bilateral pure gonadoblastoma which accounts for only 0.2% of all ovarian tumours seen at Universiti Kebangsaan Malaysia from 1980 to 1987. This tumour occurred in an 18 year old Chinese "female" who presented with primary amenorrhoea. Examination showed a phenotypic female with poorly developed external gentalia. Exploratory laparotomy revealed a hypoplastic uterus, rudimentary fallopian tubes and streak gonads. Histological examination of the gonads showed a mixed tumour comprising large germ cells and smaller sex cord derivatives arranged in characteristic nests or islands containing hyaline material.
