A Rare Case of Presacral Paraganglioma Presenting with Hypertensive Encephalopathy
- Author:
Dhiraj KB
;
Mamatha B
- Publication Type:Case Reports
- Keywords:
Presacralpararectal paraganglioma;
malignant hypertension;
hypertensive encephalopathy;
perioperative challenges;
complete excision
- MeSH:
Paraganglioma
- From:Journal of Surgical Academia
2015;5(1):54-57
- CountryMalaysia
- Language:English
-
Abstract:
Paragangliomas are exceptionally rare tumors in children of neural crest origin. Our case report represents an
extremely rare location for paraganglioma including its imaging features, perioperative challenges and
histopathological characteristics. In the present case, a 10-year-old boy had headache and blurring of vision for four
years but was not diagnosed until he came with malignant hypertension and hypertensive encephalopathy. The
symptoms raised urinary catecholamines and CT findings confirmed the diagnosis of a functioning paraganglioma in
presacral region. Challenges during surgery are to control the fluctuating blood pressure which may suddenly rise
during tumor handling and suddenly fall following its removal. The unusual location of the tumor in pararectal
region also made surgical resection difficult. Paragangliomas are rare and should be kept in mind while evaluating a
child with hypertension and complete excision is the treatment of choice.
- Full text:P020150617351831377531.pdf
