Predominant proximal upper extremity involvement in Hirayama disease
- Author:
Sung Hwa Paeng
;
Yeo Jung Kim
;
Seong-il Oh
;
Jong Seok Bae
- Publication Type:Case Reports
- MeSH:
Amyotrophy, monomelic
- From:Neurology Asia
2015;20(3):301-303
- CountryMalaysia
- Language:English
-
Abstract:
Hirayama disease usually selectively involves lower cervical myotomes (C8, T1). Thus, patients
usually manifest with atrophy and weakness of small hand muscle. Predominant isolated involvement
of proximal arm is rarely reported in Hirayama disease. Here, we report a case of Hirayama disease
who had focal weakness and wasting, mainly confined to right biceps brachii muscle, with prominent
shifting of dural sac in C4-5 segment by dynamic flexion magnetic resonance imaging (dfMRI), which
may explain this unusual distribution of the disease.
- Full text:P020151007475750425397.pdf