Schilder’s disease in a young child with tumefactive demyelinating brain lesion
- Author:
Hyo Jeong Kim
;
Sang Mi Lee
;
Heung Dong Kim
;
Joon Soo Lee
;
Hoon-Chul Kang
- Publication Type:Journal Article
- From:Neurology Asia
2013;18(4):419-421
- CountryMalaysia
- Language:English
-
Abstract:
Schilder’s disease is a rare sporadic demyelinating disease of the brain. We report a girl with Schilder’s
disease who had undergone Kasai operation for biliary atresia. The patient presented with acute right
hemiparesis. Brain magnetic resonance imaging (MRI) showed a single large tumefactive white
matter lesion. A diagnosis of Schilder’s disease was based on clinical features and MRI findings. The
patient showed dramatic clinical improvement and significant regression of the lesion in response to
high-dose intravenous methyl prednisone, and remained free of relapse of other neurologic problems
during the 3-year follow-up.
- Full text:P020150703539794859774.pdf
