Primary cutaneous anaplastic large cell lymphoma in a young woman
- Author:
Yap FBB
;
Pubalan M
- Publication Type:Case Reports
- From:Malaysian Journal of Dermatology
2008;21(-):117-119
- CountryMalaysia
- Language:English
-
Abstract:
Primary cutaneous anaplastic large cell lymphoma (ALCL) constitutes
around 1% of all cutaneous lymphomas1. It is defined as predominance
(>75%) of large clusters of CD 30+ blast like cells in the skin biopsy
with no clinical evidence of lymphomatoid papulosis, extracutaneous
localization at presentation or previous or concurrent mycosis
fungoides or other cutaneous lymphoma2. It is usually seen in males
with a median age of 40 years3. It classically presents as a solitary
ulcerated tumour on the trunk or extremities. Twenty two percent of
cases are multifocal3. Extracutaneous dissemination occurs in
approximately 10%, mainly to regional lymph nodes3. Skin restricted
disease has an excellent prognosis with 96% 5 year survival4.
Here, we report a case of primary cutaneous anaplastic large cell
lymphoma (ALCL) in a 32-year-old woman.