Mucous membrane pemphigoid
- Author:
Lee CK
;
Zuraiza MZ
;
ROKIAH I
- Publication Type:Case Reports
- Keywords:
Pemphigoid, mucous membrane
- From:Malaysian Journal of Dermatology
2009;22(-):25-27
- CountryMalaysia
- Language:English
-
Abstract:
Mucous membrane pemphigoid is a group of
putative autoimmune, chronic inflammatory,
subepithelial blistering diseases predominantly
affecting mucous membranes, characterised by
linear deposition of IgG, IgA, or C3 along the
epithelial basement membrane1. This variant of
pemphigoid is rare and encompasses a
heterogeneous group manifesting a varying
constellation of oral, ocular, skin, genital,
nasopharyngeal, oesophageal and laryngeal lesions.
In severe cases, it may lead to blindness due to
ocular involvement and may even be life
threatening due to airway obstruction. We report a
case of mucous membrane pemphigoid with oral
and genital involvement.