Spleen Rupture in Congenital Afibrinogenemia.
- Author:
Dae Yeon KIM
1
;
Seong Chul KIM
;
In Koo KIM
Author Information
1. Department of Surgery, Ulsan University College of Medicine, Seoul, Korea.
- Publication Type:Original Article
- Keywords:
Congenital afibrinogenemia;
Spleen rupture
- MeSH:
Afibrinogenemia*;
Fibrinogen;
Hemorrhage;
Humans;
Male;
Perfusion;
Rupture*;
Spleen*;
Splenectomy;
Splenic Rupture
- From:Journal of the Korean Association of Pediatric Surgeons
1999;5(2):137-140
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Congenital afibrinogenemia is a rare disorder that refers to a congenital lack of production of fibrinogen, a key component of the hemostatic system. Bleeding manifestations of congenital afibrinogenemia vary in severity from mild to catastrophic. This is a case report of splenic rupture occurred in an eight-year-old boy with congenital afibrinogenemia. A conservative treatment was carried out with perfusion of cryoprecipitate and purified virally inactivated fibrinogen concentrates and splenectomy was avoided.
