CTA in diagnosis of congenital heart disease and related heterotaxy syndrome
10.13929/j.1672-8475.201609006
- VernacularTitle:CT血管成像诊断先天性心脏病合并内脏异位
- Author:
Shali FAN
;
Jingzhe LIU
;
Dong LIU
;
Ying ZHANG
;
Haisheng ZHANG
;
Xinyu LIU
- Keywords:
Heterotaxy;
Isomerism;
Tomography,X-ray computed;
Angiography
- From:
Chinese Journal of Interventional Imaging and Therapy
2017;14(3):155-158
- CountryChina
- Language:Chinese
-
Abstract:
Objective To evaluate the value of CTA in assessing congenital heart disease and related heterotaxy syndrome.Methods A total of 20 patients with congenital heart disease and heterotexy syndrome underwent CTA and 3-dimensional reconstructions.And intracardiac and extracardiac abnormalities were assessed.Results Three cases were left isomerism,two of which were bi-lobed left lungs and trilobed right lungs,and another one was bi-lobed lungs.The most common associated cardiovascular anomalies included single ventricle (n=2),atrial septal defect (n=2),ventricular septal defect (n=1),transposition of the great arteries (n=2),pulmonary artery stenosis (n=2),atresia (n=1),persistent left superior vena (n=1),no hepatic segment of inferior vena cava (n=1).The rest 17 cases were right isomerism.All of them were trilobed lungs.Associated cardiovascular anomalies included single ventricle (n=9),double outlet of right ventricle (n=2),endocardial cushion defect (n=6),atrial septal defect (n=10),patent foramen ovale (n=1),ventricular septal defect (n =8),transposition of the great arteries (n =14),pulmonary artery stenosis (n =16),atresia (n =1),pulmonary venous drainage (n=6),persistent left superior vena (n=7),no hepatic segment of inferior vena cava (n=2).Conclusion CTA can clearly show the structure of heart,great vessels,chest and abdomen which is a useful tool to accurately assess congenital heart disease and related heterotaxy syndrome for medical or surgical management.
