A Case of Adult-onset Rasmussen's Encephalitis Responsive to High-dose Steroid and Antiepileptic Medication.
- Author:
Soon Keum LEE
1
;
Min Cheol JUN
;
Kwang Deog JO
;
Soo Bin IM
Author Information
1. Department of Neurology, Gangneung Asan Hospital, University of Ulsan College of Medicine, Korea. soonklee@knh.co.kr
- Publication Type:Case Report
- Keywords:
Rasmussen encephalitis;
Steroid;
Antiepileptic drugs
- MeSH:
Anticonvulsants;
Aphasia;
Encephalitis*;
Epilepsy;
Female;
Generalization (Psychology);
Humans;
Middle Aged;
Paresis;
Seizures
- From:Journal of the Korean Neurological Association
2004;22(1):67-70
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Rasmussen's encephalitis is a rare autoimmune disorder characterized by intractable epilepsy and progressive unilateral hemispheric dysfunction as well as mental deterioration. Although the disorder typically begins in childhood, a few cases have been reported with symptom onset in adulthood showing variable clinical characteristics. We report a 63-year-old woman with adult-onset partial seizure with intermittent secondary generalization, progressive right hemiparesis, and aphasia, who showed positive response to high-dose steroid and antiepileptic drugs.