Spontaneous renal artery dissection in Ehlers-Danlos syndrome.
10.12701/yujm.2016.33.1.44
- Author:
Byung Hun LIM
1
;
Song I LEE
;
Jae Hong LIM
;
Su Jin OH
;
Min Su CHU
;
Seon Ho AHN
;
Seung Jae BYUN
Author Information
1. Department of Internal Medicine, Wonkwang University School of Medicine, Iksan, Korea. ashneph@wonkwang.ac.kr
- Publication Type:Case Report
- Keywords:
Ehlers-Danlos syndrome;
Renal artery;
Spontaneous dissection
- MeSH:
Angiography;
Arteritis;
Connective Tissue;
Ehlers-Danlos Syndrome*;
Fibromuscular Dysplasia;
Flank Pain;
Hand Joints;
Joints;
Korea;
Marfan Syndrome;
Neurofibromatoses;
Polyarteritis Nodosa;
Renal Artery*;
Skin;
Tuberculosis
- From:Yeungnam University Journal of Medicine
2016;33(1):44-47
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Primary dissection of the renal artery is rare. Spontaneous renal artery dissection can be associated with diseases such as medial degeneration, neurofibromatosis, syphilitic arteritis, tuberculosis, polyarteritis nodosa, Marfan syndrome, fibromuscular dysplasia, or Ehlers-Danlos syndrome (EDS). Among these causes, EDS related renal artery dissection is very rare worldwide and has not been previously reported in Korea. EDS are a group of heritable connective tissue disorders characterized by fragility of the skin and hypermobility of the joints. We describe the case history of a young man who presented with left side flank pain, hypermobility of the hand joints and showed left renal artery dissection on computed tomography and angiography that turned out to be the first complication of vascular type EDS.
