Renal and hepatic angiomyolipoma and renal failure in two cases of tuberous sclerosis.
- Author:
Dong Won LEE
;
Dong HOU
;
Hyung Ok KIM
;
Chung Won KIM
- Publication Type:Original Article
- Keywords:
Angiomyolipoma;
Tuberous sclerosis
- MeSH:
Angiomyolipoma*;
Dialysis;
Hamartoma;
Humans;
Kidney;
Lipoma;
Liver;
Nephrectomy;
Renal Insufficiency*;
Sclerosis;
Tomography, X-Ray Computed;
Tuberous Sclerosis*
- From:Korean Journal of Dermatology
1992;30(1):109-114
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
The abdominal manifestations of tuberous sclerosis are most frequently related to hamartomas of the kidneys which are readily detectable on CT scans because of their fat content. However, lipomas or angiomyolipomas of the liver are quite rare. Two patients with angiomyolipomas of the kidney had typical kin lesions of tuberous sclerosis. Orie had been on long-term dialysis for chronienal failure due to an angiomyolipomatous lesions and the other had undergone nephrectomy because of nonfunction kidney. Hepatic hamartomas were also seen in both atients. We should anticipate that such masses are not infrequent with uberous sclerosis.
