Arrhythmogenic Noncompaction Cardiomyopathy: Is There an Echocardiographic Phenotypic Overlap of Two Distinct Cardiomyopathies?.
10.4250/jcu.2015.23.3.186
- Author:
Dursun ARAS
1
;
Ozcan OZEKE
;
Serkan CAY
;
Firat OZCAN
;
Kazim BASER
;
Umuttan DOGAN
;
Murat UNLU
;
Burcu DEMIRKAN
;
Omac TUFEKCIOGLU
;
Serkan TOPALOGLU
Author Information
1. Department of Cardiology, Turkiye Yuksek Ihtisas Training and Research Hospital, Ankara, Turkey. ozcanozeke@gmail.com
- Publication Type:Case Report
- Keywords:
Arrhythmogenic cardiomyopathy;
Noncompaction cardiomyopathy
- MeSH:
Adult;
Arrhythmogenic Right Ventricular Dysplasia;
Atrioventricular Block;
Cardiomyopathies*;
Diagnosis;
Echocardiography*;
Humans
- From:Journal of Cardiovascular Ultrasound
2015;23(3):186-190
- CountryRepublic of Korea
- Language:English
-
Abstract:
The clinical diagnosis of right ventricular (RV) cardiomyopathies is often challenging. It is difficult to differentiate the isolated left ventricular (LV) noncompaction cardiomyopathy (NC) from biventricular NC or from coexisting arrhythmogenic ventricular cardiomyopathy (AC). There are currently few established morphologic criteria for the diagnosis other than RV dilation and presence of excessive regional trabeculation. The gross and microscopic changes suggest pathological similarities between, or coexistence of, RV-NC and AC. Therefore, the term arrhythmogenic right ventricular cardiomyopathy is somewhat misleading as isolated LV or biventricular involvement may be present and thus a broader term such as AC should be preferred. We describe an unusual case of AC associated with a NC in a 27-year-old man who had a history of permanent pacemaker 7 years ago due to second-degree atrioventricular block.
