Surgical Treatment of Acute Type A Aortic Dissection in Ehlers-Danlos Syndrome.
- Author:
Dong Seop JEONG
1
;
Kyung Hwan KIM
;
Hyuk AHN
Author Information
1. Department of Thoracic and Cardiovascular Surgery, Seoul National University College of Medicine, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Ehlers-Danlos syndrome;
Aortic dissection;
Aortic aneurysm, arcending
- MeSH:
Ehlers-Danlos Syndrome*;
Hemorrhage;
Skin
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2000;33(11):910-914
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Ehlers-Danlos syndrome type IV(the arterial-ecchymotic type) which has skin fragility, easy bruisability, and j oint hyperextensibility is occasionally combined with large vessel involve-ment and spontaneous catastrophic bleeding. As even a small inj ury can cause profound vascular tearing and damage, surgical management is hazardous and often unrewarding. We report a successful surgical treatment of an acute type A aortic dissection associated with Ehlers-Danlos syndrome.
