Anomalous Origin of the Left Coronary Artery from the Pulmonary Artery : Report of an Adult Case.
- Author:
Taeyeun KIM
1
;
Seo Jin JEA
;
Gi Young JANG
;
Chang Sung SON
;
Joo Won LEE
;
Yong Jin KIM
Author Information
1. Department of Pediatrics, College of Medicine, Korea University, Seoul, Korea. jgynhg@dreamwiz.com
- Publication Type:Case Report
- Keywords:
Anomalous origin of the left coronary artery from the pulmonary artery;
Bland-White-Garland syndrome;
Adult
- MeSH:
Adult*;
Bland White Garland Syndrome;
Camelids, New World;
Coronary Vessels*;
Diagnosis;
Heart Failure;
Humans;
Infarction;
Mitral Valve Insufficiency;
Myocardial Ischemia;
Pulmonary Artery*;
Young Adult
- From:Journal of the Korean Pediatric Cardiology Society
2007;11(3):235-239
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA), also termed Bland-White-Garland syndrome, is a rare congenital cardiac anomaly characterized by myocardial ischemia which becomes symptomatic during early infancy leading to infarction, left heart failure or even death. More than 90% of patients can be dead within first year of life if untreated, so adult type ALCAPA without surgical correction is quitely rare. We present a case of a 20-year-old man with ALPACA syndrome whose diagnosis took several years to be made because he was mistaken to have organic mitral regurgitation.
