Experience in corrective surgery for Ebstein's anomaly of 139 cases
- VernacularTitle:Ebstein心脏畸形139例手术治疗经验
- Author:
Renfu ZHANG
;
Zengwei WANG
;
Hongyu ZHU
- Publication Type:Journal Article
- Keywords:
Ebstien's anomaly Heart valve prosthesis implantation Tricuspid valve plasty
- From:
Chinese Journal of Thoracic and Cardiovascular Surgery
2003;0(01):-
- CountryChina
- Language:Chinese
-
Abstract:
Objective: To summarize the experience of corrective surgery for Ebstein's anomaly. Methods: 139 patients with Ebstein's anomaly were operated on from June, 1980 to January, 2000. Among them, 111 cases received atrialized ventricle plication, tricuspid valve plasty and Devega tricuspid annuloplasty, 27 cases undergoing tricuspid valve replacement. One case of right ventricular hypoplasia received extra total cavopulmonary connection (ETCPC). Results: In the whole group, there were 12 operative deaths, with mortality rate of 8.6%. While in the later 10 years, operative mortality rate was reduced to 3.3%. In the group of plastive operation, 10 cases were re-operated with valve replacement and all were survived. Conclusion: Operative method of Ebstein's anomaly should be decided according to the pathologicoanatomic feature. For mild type, tricuspid valve plasty should be chosen. For medium A type, plastic operation should be performed. For medium B type, plasty or valve replacement should be cautiously selected. For severe type, valve replacement should be considered.