Degos' disease:A case report and review of literature
- VernacularTitle:恶性萎缩性丘疹病并发肠穿孔1例并文献综述
- Author:
Xianwei WANG
;
Xi LIU
;
Zhen ZENG
;
Yixiong LI
- Publication Type:Journal Article
- Keywords:
Malignant atrophic papulosis;
Intestinal perforation;
Vasculitis
- From:
Journal of Peking University(Health Sciences)
2003;0(04):-
- CountryChina
- Language:Chinese
-
Abstract:
A 18-year-old male patient's case was diagnosed as Degos'disease with pathognomonic skin lesions,accompanied by small bowel perforation,and reported here. Skin histopothological test show that the typical wedge-shaped necrobiosis and lymphocyte inflammatory infiltration. Vessels showed narrowing and thrombosis,with lymphocyte infiltration. Degos'disease is a systemic necrotizing vasculitis. Skin biopsy can confirm its diagnosis. Severe systemic complication should be prevented. Degos'disease should be considered in the differential diagnosis of skin lesions associated with systemic involvement.
