Idiopathic Hypertrophic Pachymeningitis in the Craniocervical Junction.
10.14245/kjs.2015.12.3.169
- Author:
Jin Hyuk BANG
1
;
Keun Tae CHO
;
Eo Jin KIM
Author Information
1. Department of Neurosurgery, Dongguk University Ilsan Hospital, Goyang, Korea and Dongguk University, Seoul, Korea. ktcho21@naver.com
- Publication Type:Case Report
- Keywords:
Idiopathic hypertrophic pachymeningitis;
Craniocervical junction;
Diagnosis;
Treatment
- MeSH:
Diagnosis;
Dura Mater;
Fibrosis;
Meningitis*;
Rare Diseases;
Spinal Cord
- From:Korean Journal of Spine
2015;12(3):169-172
- CountryRepublic of Korea
- Language:English
-
Abstract:
Idiopathic hypertrophic pachymeningitis (IHP) is a rare disease, and it is characterized by chronic progressive inflammatory fibrosis and thickening of the dura mater with resultant compression of the spinal cord or neural structure without any identifiable cause. It can occur in the intracranial or spinal dura mater alone or as a craniospinal form. The spinal form is rarer than the cranial form and the craniospinal form is extremely rare. We report a rare case of IHP in the craniocervical junction involving both the cranial and spinal dura mater and discuss the diagnosis and management of the disease.
