A Case of Clear Cell Sarcoma of the Kidney.
- Author:
Sun Young PARK
1
;
So Young SUL
;
Min Seop SONG
;
Woo Yeong CHUNG
;
Soon Yong LEE
Author Information
1. Department of Pediatrics, College of Medicine, Pusan Paik Hospital, Inje University, Pusan, Korea.
- Publication Type:Case Report
- Keywords:
Clear cell sarcoma;
Kidney
- MeSH:
Brain;
Drug Therapy;
Female;
Follow-Up Studies;
Humans;
Infant;
Kidney*;
Neoplasm Metastasis;
Nephrectomy;
Physical Examination;
Recurrence;
Ribs;
Sarcoma, Clear Cell*;
Thorax;
Wilms Tumor
- From:Korean Journal of Nephrology
1997;16(3):620-624
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Clear cell sarcoma of the kidney(CCSK) is one of the rare malignant renal tumors in childhood and is different from Wilms tumor by its pathologic features, clinical manifestations and propensity to metastasize to the skeletal system and brain. We report a case of CCSK on the right kidney in a 14-month-old girl presented with abdominal distention and palpable huge abdominal mass on physical examination, followed by metastasis to the rib on the left upper thorax. After right nephrectomy, chemotherapy with National Wilms Tumor Study DD regimen(vincristine+dactinomycin+adriamycin) was continued without any evidence of relapse until the last follow-up, 1 year after beginning chemotherapy. A brief review of related literatures was made.
