A Case of Neurofibromatosis associated with Pseudoatrophic Macules.
- Author:
Min KIM
;
Seong Jin KIM
;
Seung Chul LEE
;
Young Ho WON
- Publication Type:Original Article
- Keywords:
Neurofibroma;
Neurofibromatosis;
Pseudoatrophic macule
- MeSH:
Collagen;
Congenital Abnormalities;
Dermis;
Eccrine Glands;
Humans;
Korea;
Male;
Neurofibroma;
Neurofibromatoses*;
Spine;
Young Adult
- From:Korean Journal of Dermatology
2000;38(3):372-375
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
We report a case of Neurofibromatosis in a 19-year-old male who showed a pinkish atrophic patch on the back. He presented with multiple caf au lait macules, neurofibromas and axillary freckling. Cervical and thoracic spine X-ray revealed wedge-shaped bony deformities due to neurogenic tumor involving the vertebral foramina. Histopathologic examination demonstrated dilated vessels in the papillary dermis, decreased collagen in the reticular dermis and entrapped eccrine gland. This case suggests pseudoatrophic macule should be regarded to be a rare cut manifestation in neurofibromatosis. To our best knowledge, this is the first report in korea to show atrophic patch in neurofibromatosis.
