Primary Intimal Sarcoma Originating from Pulmonary Valve.
- Author:
Jae Won LEE
;
Sang Wan RYU
;
Suk Jung CHOO
;
Hyun SONG
;
Myeung Gun SONG
- Publication Type:Case Report
- MeSH:
Cough;
Drug Therapy;
Dyspnea;
Edema;
Female;
Humans;
Middle Aged;
Neoplasm Metastasis;
Pulmonary Artery;
Pulmonary Embolism;
Pulmonary Valve*;
Radiotherapy;
Rare Diseases;
Sarcoma*;
Tomography, X-Ray Computed
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2000;33(10):823-826
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Primary intimal sarcoma of the pulmonary artery is a rare disease and there has been no report of any case originating from the pulmonary valve. Recently we experienced a 62 year-old female patient who had a primary intimal sarcoma of the pulmonary valve with distal metastasis. She was brought to medical attention due to exertional dyspnea facial edema productive coughing and general weakness for 1 month. Chest CT and echocardi-ography suggest an acute pulmonary thromboembolism or tumor. Exploration showed a large polypoid mass arising from the pulmonary leaflets and multiple masses on distal pulmonary arteries. We replaced the pulmonary valve and reconstructed the pulmonary artery. She received radiotherapy 1 month postoperatively and now 4 months after surgery she has begun receiving chemotherapy.
