Intraosseous Arteriovenous Malformation of the Sphenoid Bone Presenting with Orbital Symptoms Mimicking Cavernous Sinus Dural Arteriovenous Fistula: A Case Report.
10.7461/jcen.2013.15.3.251
- Author:
Eun Suk PARK
1
;
Young Jin JUNG
;
Jung Ho YUN
;
Jae Sung AHN
;
Deok Hee LEE
Author Information
1. Department of Neurosurgery, Ulsan University Hospital, University of Ulsan College of Medicine, Ulsan, Korea.
- Publication Type:Case Report
- Keywords:
Arteriovenous malformations;
Hemangioma;
Primary intraosseous vascular malformation;
Klippel-Trenaunay-Weber syndrome
- MeSH:
Adult;
Angiography;
Arteriovenous Malformations;
Cavernous Sinus;
Caves;
Central Nervous System Vascular Malformations;
Exophthalmos;
Female;
Hemangioma;
Humans;
Klippel-Trenaunay-Weber Syndrome;
Lower Extremity;
Mandible;
Maxilla;
Orbit;
Sphenoid Bone
- From:Journal of Cerebrovascular and Endovascular Neurosurgery
2013;15(3):251-254
- CountryRepublic of Korea
- Language:English
-
Abstract:
Intraosseous arteriovenous malformation (AVM) in the craniofacial region is rare. When it occurs, it is predominantly located in the mandible and maxilla. We encountered a 43-year-old woman with Klippel-Trenaunay syndrome affecting the right lower extremity who presented with a left orbital chemosis and proptosis mimicking the cavernous sinus dural arteriovenous fistula. Computed tomography angiography revealed an intraosseous AVM of the sphenoid bone. The patient's symptoms were completely relieved after embolization with Onyx. We report an extremely rare case of intraosseous AVM involving the sphenoid bone, associated with Klippel-Trenaunay syndrome.