Sturge-Weber Syndrome:Imaging Diagnosis(A Report of 11 Cases and a Review of the Literature
- VernacularTitle:Sturge-Weber综合征的影像学诊断(附11例报告及文献复习)
- Author:
Jizhou YANG
;
Shuquan MIAO
;
Dapeng SHI
- Publication Type:Journal Article
- Keywords:
brain;
sturge-weber syndrome;
imagiology
- From:
Journal of Practical Radiology
2001;0(08):-
- CountryChina
- Language:Chinese
-
Abstract:
Objective To study imaging findings of Sturge-Weber syndrome. Methods The clinical manifestations and imaging findings of 11 cases suffered from Sturge-Weber syndrome were analysed. 10 cases had facial vascular nerves angioma in the trigeminal nerve distribation. Routine CT examination was performed in all 11 cases, 2 cases had head radiography and 8 cases had MRI, 5 cases had enhanced CT and 3 cases had enhanced MRI.Results Imaging finding included:on the affected hemisphere, cortical calcifications (n=11), brain atrophy (n=9), the interfaces between gray matter and white matter blured, dilated subependymal veins,enlargeel choroids plexus (n=7) and increasing thickness of cranial diploe (n=8). The choroids plexus of lateral ventricle was prominent enhanced in 5 cases. Enhancement of cortical areas and vessels on the surface of brain were noted in 6 cases. Conclusion Head radiography has finite effects in the diagnosis of Sturge-Weber syndrome, MRI combined with CT plays an important role in the diagnosis of this syndrome.