Cochlear Nerve Deficiency in a Child with Auditory Neuropathy
- VernacularTitle:耳蜗神经发育异常的小儿听神经病
- Author:
Jinling WANG
;
Yi HUAN
;
Lei GAO
;
Juan XIE
- Publication Type:Journal Article
- Keywords:
Auditory neuropathy;
Audiometry;
Cochlear nerve;
Magnetic resonance imaging
- From:
Journal of Audiology and Speech Pathology
1998;0(02):-
- CountryChina
- Language:Chinese
-
Abstract:
Objective To explore the auditory neuropathy(AN) characteristics in a child with cochlear nerve deficiency.Methods Audiological test,HRCT image and HRMRI from this child were analyzed.Results ABR responses were absent from the both ears while normal DPOAE in the right ear was noted with abnormal DPOAE at some frequencies in the left.The neural responses from the right cochlea were absent but weak responses were noted in the left by means of the oblique sagittal MRI on the internal auditory canal.Conclusion The child with cochlear nerve deficiency can present with electrophysiological evidence of AN.The cochlear nerve deficiency was considered about the main site of lesion and one of the etiology of AN.The inclined sagittal MRI scanning plays a very important role in assessing cochlear nerve deficiency.