Crystalline Retinopathy without Corneal Dystrophy.
- Author:
Hyun Dong KIM
1
;
Man Seong SEO
Author Information
1. Department of Ophthalmology, Chonnam National University Medical School & Hospital, Kwangju, Korea.
- Publication Type:Original Article
- Keywords:
Intraretinal crystal;
Retinal pigment epithelial dystrophy;
Choroidal sclerosis
- MeSH:
Choroid;
Cornea;
Crystallins*;
Female;
Fingers;
Follow-Up Studies;
Humans;
Lipid Metabolism;
Middle Aged;
Retinaldehyde;
Retinitis Pigmentosa;
Sclerosis;
Visual Acuity
- From:Journal of the Korean Ophthalmological Society
2000;41(6):1445-1450
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Bietti's crystalline retinopathy is a rare form of tapetoretinal degeneration characterized by yellow, polygonal, glistening intraretinal crystals in the posterior pole and in the superficial paralimbal cornea, which may be due to a systemic abnormality of lipid metabolism, and has been to have a autosomal recessive pattern.Also lots of the reports described similar cases without any corneal changes. 56 years-old female with complaint of progressive visual decrease had corrected visual acuity of 0.1 in her right eye and 1.0 in her left eye.Yellow intraretinal crystals with retinal pigment epithelial (RPE)dystrophy and choroidal sclerosis were noticed without any corneal changes.During follow-up for thirty months, visual acuity gradually decreased to counting fingers in her right eye and 0.7 in her left eye, and RPE degeneration and choroidal sclerosis worsened with no change in intraretinal crystals.
