Diagnosis and therapy of familial adenomatous polyposis with desmoid tumour
- VernacularTitle:家族性腺瘤性息肉病伴发硬纤维瘤的诊断和治疗
- Author:
Enda YU
;
Zheng LOU
;
Xiaodong XU
;
Ronggui MENG
;
Hao WANG
;
Guoxiang JIN
;
Chuangang FU
- Publication Type:Journal Article
- Keywords:
Adenomatous polyposis coli;
Fibromatosis,aggressive;
Diagnosis;
Therapeutics
- From:
Chinese Journal of General Surgery
1993;0(03):-
- CountryChina
- Language:Chinese
-
Abstract:
Objective To summarize the experience in diagnosis and therapy of familial adenomatous polyposis with desmoid tumour. Methods Clinical data of 6 patients with familial adenomatous polyposis and desmoid tumour from Jan 1989 to Jan 2005 were retrospectively analyzed. Results Five patients received proctocolectomy and 1 abdominoperineal resection. The most common symptom was progressive painless mass in abdomen. All patients were confirmed by image examination. Four received surgery, 2 were treated by medicine postoperatively and 1 got watchful therapy. Postoperative recurrence developed in two cases and one suffered from short bowel syndrome. All patients were alive at the follow-up. Conclusions FAP with desmoid tumour is not a rare condition and we should pay attention to diagnosis and manage this disease entity. A reasonable remedy was selected according to general state of health and location of desmoid tumour which can improve prognosis and quality of life.
