Clinical features and surgical treatment of retroperitoneal Castleman′s disease with paraneoplastic pemphigus
- VernacularTitle:腹膜后Castleman病伴副肿瘤天疱疮的临床特征及外科治疗
- Author:
Lanbo ZHANG
;
Yinhua LIU
;
Bin WANG
;
Jing WANG
;
Xuejun ZHU
- Publication Type:Journal Article
- Keywords:
Pemphigus, paraneoplastic;
Giant lymph node hyperplasia;
Surgical procedures, operative
- From:
Chinese Journal of General Surgery
1993;0(03):-
- CountryChina
- Language:Chinese
-
Abstract:
Objective To investigate the clinical characteristics and surgical treatment of retroperitoneal Castleman′s disease (CD) with paraneoplastic pemphigus (PNP).Methods The clinical symptoms, laboratory, histopathologic, CT findings and results of surgery in 7 patients were evaluated.Results All of 7 patients presented with PNP.Retroperitoneal tumors were found by CT examination and surgically removed.Castleman disease was confirmed by histopathology.Reoperation was performed to resect the recurrent tumor in one patient.The signs of PNP were dissolved completely or partially after operation.Conclusion Retroperitoneum CD with PNP are characteristic of distinctive clinical features.Surgical excision improves the mucocutanous manifestation of PNP.