A case of peritoneal desmoplastic small round cell tumor.
- Author:
Ki Yeol YANG
1
;
Young Sun KIM
;
Ji Hyun HAN
;
Yong Ku PARK
;
Min Hyung JUNG
Author Information
1. Department of Obstetrics and Gynecology, Kyung Hee Medical Center, School of Medicine, Kyung Hee University, Seoul, Korea. webhospital@naver.com
- Publication Type:Case Report
- Keywords:
Desmoplastic small round cell tumor;
Peritoneum
- MeSH:
Adult;
Cytogenetics;
Desmoplastic Small Round Cell Tumor;
Female;
Humans;
Male;
Peritoneum;
Survival Rate
- From:Korean Journal of Obstetrics and Gynecology
2009;52(3):377-381
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Desmoplastic small round cell tumor is a rare and aggressive tumor that affects young males. It is usually an abdominopelvic malignancy that demonstrates distinct histological appearances and a unique cytogenetic profile. There have been many different approaches to the treatment of desmoplastic small round cell tumor, but unfortunately it remains incurable and has poor long-term survival rates. However, with an aggressive approach to the treatment using multiple modalities, some temporary benefit to survival can be achieved. There has not yet been a case in which treatment has led to a curative outcome. Recently, we also experienced a case of very poor outcome of 31-year-old female with small round cell tumor in peritoneum. Here, we report the case with a brief review of literatures.
