Living-related liver transplantation for the treatment of Wilson's disease
- VernacularTitle:亲体部分肝移植治疗Wilson病20例报告
- Author:
Feng ZHANG
;
Xuehao WANG
;
Xiangcheng LI
;
Jun LIU
;
Hongbo QIN
- Publication Type:Journal Article
- Keywords:
Hepatolenticular degeneration;
Liver transplantation;
Living donors;
Postoperative complications
- From:
Chinese Journal of General Surgery
2001;0(08):-
- CountryChina
- Language:Chinese
-
Abstract:
Objective To evaluate living-related liver transplantation (LRLT) for the treatment of Wilson′s disease. MethodsBetween Jan. 2001 and Oct. 2003,LRLT was performed in 20 patients (mean age 11.1 years) of late staged Wilson′s disease. Among them emergency transplantation was performed in 3 patients. Donor livers were all from patient′s parents. ResultsSurgery was successful in all donors and recipients, liver function test and serum ceruloplasmin reached normal level one month after transplantation. One patient died of severe rejection. Discharged patients were followed up from 2~33 months (mean 18.9 months). [WT5”HZ]ConclusionsLiving related liver transplantation is an effective treatment for Wilson′s disease complicated with hepatic dysfunction.