Fetal Cardiac Rhabdomyoma Diagnosed by Ultrasonography and Its Relation with Tuberous Sclerosis
- VernacularTitle:超声诊断胎儿心脏横纹肌瘤及其与结节性硬化症的关系
- Author:
Ling YAO
;
Yan CHEN
;
Qingqing WU
- Publication Type:Journal Article
- Keywords:
Fetal;
Heart neoplasms;
Rhabdomyoma;
Tuberous sclerosis;
Ultrasonography, prenatal
- From:
Chinese Journal of Perinatal Medicine
1998;0(03):-
- CountryChina
- Language:Chinese
-
Abstract:
Objective To study the possibility of fetal cardiac rhabdomyoma diagnosed by ultrasonography,and the relationship between the fetal cardiac rhabdomyoma and family tuberous sclerosis. Methods High resolution ultrasonic equipment with fetal cardiac software was used. The main cross section of four chamber view was studied mainly. The location, the number of the tumor and the outflow tract of left and right ventricular cordis were scanned carefully, the maternal abdominal scan was performed as well. Results Five cases of fetal cardiac rhabdomyoma were found by routine prenatal ultrasonography, and were confirmed by autopsy. Among them, one case were associated with maternal tuberous sclerosis. Conclusions Fetal cardiac rhabdomyoma associated with tuberous sclerosis. Fetus with cardiac rhabdomyoma frequently die of cardiac failure; since the prognosis of the tuberous sclerosis with neural sclerosis was very poor, when the fetal cardiac rhabdomyoma was detected prenatally, the possibility of tuberous sclerosis should be considered, also relative examination must be performed to the mother to decrease the perinatal mortality.