A Case of Hemophagocytic Syndrome with Terminal Ileal Ulcerations.
- Author:
Jae Hyun MOON
1
;
Sung Pyo HONG
;
Pil Won PARK
;
Kwang Hyun KO
;
Seong Gyu HWANG
;
Kyu Sung RIM
;
Hee Jung AN
;
Myung Seo KANG
Author Information
1. Departments of Internal Medicine, Bundang CHA Hospital, Pochon CHA University, Seongnam, Korea. sphong@cha.ac.kr
- Publication Type:Case Report ; English Abstract
- Keywords:
Hemophagocytic syndrome;
Terminal ileal ulcer
- MeSH:
Adult;
Fatal Outcome;
Humans;
Ileal Diseases/complications/*diagnosis;
Lymphohistiocytosis, Hemophagocytic/complications/*diagnosis/pathology;
Male;
Tomography, X-Ray Computed;
Ulcer/complications/*diagnosis
- From:The Korean Journal of Gastroenterology
2006;48(3):205-209
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Reactive hemophagocytic syndrome or hemophagocytic lymphohistiocytosis, is characterized by the proliferation of benign histiocytes showing phagocytosis of blood cells in hematopoietic organs including bone marrow, spleen, or lymph nodes, accompanied by fever, hepatosplenomegaly, hepatic dysfunction, pancytopenia, and hypertriglyceridemia. The pathogenesis of reactive hemophagocytic syndrome is unknown. It is often associated with infection, malignant neoplasm, autoimmune disease, drugs and various immunodeficiencies. The prognosis of this syndrome is poor and the causes of death are hemorrhage, infection, or multiorgan failure. We experienced a case of hemophagocytic syndrome with terminal ileal ulcers, not associated with other causes. Thus, we report this case with a review of literatures.
