The treatment progress of liver tansplantation for hepatolenticular degeneration
10.3760/cma.j.jssn.1673-4904.2016.09.026
- VernacularTitle:肝豆状核变性的肝移植治疗新进展
- Author:
Baga SHAN
;
Zhilei SU
;
Guochao ZHANG
;
Feng QI
;
Dehai WU
;
Sheng TAI
- Publication Type:Journal Article
- Keywords:
Hepatolenticular degeneration;
Liver transplantation;
Metabolic diseases
- From:
Chinese Journal of Postgraduates of Medicine
2016;39(9):855-857
- CountryChina
- Language:Chinese
-
Abstract:
Hepatolenticular degeneration was one of the rare several genetic metabolic diseases in clinic that could be cured by liver transplantation method, developing slowly and being irreversible. Metabolic disorders of copper lead to abnormal copper accumulation in various of tissues and organs. So that, the disease′s clinical manifestations were lacking in specificity and many patients missed the best opportunity of drug treatment. With the maturity of technologies and innovation of theory of liver transplantation, there were more and more methods that will be applied to personalized treatment. In this paper, a review of the research progress in the treatment of hepatolenticular degeneration with liver transplantation was made with reference to the relevant literature at home and abroad.
