Isolated Right Ventricular Noncompaction Accompanied by Right Ventricular Failure.

Author: Sanghyok LIM ¹ ; Jihun AHN ; Taehun O ; Donghyun LEE ; Minwoo PARK
Author Information

1. Department of Internal Medicine, Soonchunhyang University Cheonan Hospital, Soonchunhyang University College of Medicine, Cheonan, Korea.
Publication Type:Case Report
Keywords: Right ventricular noncompaction; Echocardiography; Right-sided heart failure
MeSH: Calcium Channels; Cardiomyopathies; Diagnosis; Digitalis; Diuretics; Echocardiography; Embryonic Development; Female; Heart Failure; Heart Ventricles; Humans; Male; Myocardium; Pregnancy; Prescriptions; Ventricular Function, Right
From:Korean Journal of Medicine 2015;88(1):69-73
CountryRepublic of Korea
Language:English
Abstract: Noncompaction of the ventricular myocardium is a rare congenital cardiomyopathy caused by arrest of normal endomyocardial embryogenesis. Isolated right ventricular noncompaction (IRNC) is an even rarer form of this disease. We report herein on a 68 year-old male diagnosed with IRNC who presented with right-sided heart failure, without involvement of the left ventricle. Diagnosis was achieved with the aid of echocardiography and ventriculography. Medical treatment including prescription of diuretics, a calcium channel blocker, and digitalis, improved both the symptoms and right ventricular function.