Clinical advances of hemophagocytic syndrome
10.3760/cma.j.issn.1671-7368.2016.07.020
- VernacularTitle:噬血细胞综合征的临床诊治进展
- Author:
Yanfang LIU
;
Jianhua ZHANG
;
Linhua YANG
- Publication Type:Journal Article
- Keywords:
Lymphohistiocytosis hemophagocytic;
Diagnosis;
Treatment
- From:
Chinese Journal of General Practitioners
2016;15(7):565-568
- CountryChina
- Language:Chinese
-
Abstract:
Hemophagocytic syndrome is a group of fatal immune function disorder,which can be divided into primary and secondary HPS.The disease is complex,lacking of specificity,difficult in diagnosis with quick progress,high mortality and poor prognosis.The diagnosis is mainly based on the HPS-2004 diagnostic criteria,etoposide,dexamethasone and cyclosporine would be first chosen for treatment.This article reviews the clinical advances on etiology,diagnosis,treatment and prognosis of hemophagocytic syndrome.