Anesthetic management of a patient with Huntington's chorea: A case report.
10.4097/kjae.2013.64.3.262
- Author:
Jong Man KANG
1
;
Jun Young CHUNG
;
Jin Hee HAN
;
Yung Suk KIM
;
Bong Jae LEE
;
Jae Woo YI
Author Information
1. Department of Anesthesiology and Pain Medicine, Kyung Hee University Hospital at Gangdong, College of Medicine, Kyung Hee University, Seoul, Korea. mdyjwchk@khu.ac.kr
- Publication Type:Case Report
- Keywords:
Bronchoscope;
Huntington disease;
Intubation
- MeSH:
Anesthesia, General;
Bronchoscopes;
Chorea;
Dementia;
Emergencies;
Humans;
Huntington Disease;
Intubation;
Nervous System;
Pharyngeal Muscles;
Sodium;
Succinylcholine;
Thiopental
- From:Korean Journal of Anesthesiology
2013;64(3):262-264
- CountryRepublic of Korea
- Language:English
-
Abstract:
Huntington's chorea is a rare hereditary disorder of the nervous system. It is inherited as an autosomal dominant disorder and is characterized by progressive chorea, dementia and psychiatric disturbances. The best anesthetic technique is yet to be established for these patients with increased risk of aspiration due to involvement of pharyngeal muscles and an exaggerated response to sodium thiopental and succinylcholine. The primary goal in general anesthesia for these patients is to provide airway protection and a rapid and safe recovery. We report the anesthetic management of a 51-year-old patient with Huntington's chorea admitted for an emergency operation.
