A Case of Benign Nonte ratoid Medulloepithelioma of the Optic Nerve Head.
- Author:
Jung Hwan KIM
1
;
Eon Sup PARK
;
Han Nam YANG
Author Information
1. Department of Ophthalmology, College of Medicine, Chung-ang University.
- Publication Type:Case Report
- Keywords:
Medulloepithelioma;
Optic nerve head
- MeSH:
Child, Preschool;
Ciliary Body;
Epithelium;
Female;
Humans;
Korea;
Neuroectodermal Tumors, Primitive*;
Optic Disk*;
Optic Nerve*;
Retina;
Strabismus
- From:Journal of the Korean Ophthalmological Society
1999;40(6):1727-1731
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Medulloepithelioma(diktyoma) is a uncommon congenital tumor that is generally believed to arise from the embryonic neuroepithelium of the medullary tube. This tumor usually arises from the ciliary body epithelium. But medulloepitheliomas of the retina and optic nerve may also occur, although it is extremely rare, because the embryonal medullary epithelium that lines the optic vesicle is continuous with the epithelium lining the cavity of the optic nerve during the early embryonal period. The occurrence of medulloepithelioma of the optic nerve is exceptionally rare, with only a few cases have been previously reported. We report a first case of medulloep-ithelioma of the optic nerve head in Korea in a 5-year-old girl who presented with a poor vision and squint of the left eye.
