Surfactant protein C gene mutations associated with children interstitial lung disease
10.3760/cma.j.issn.1673-4408.2016.03.008
- VernacularTitle:表面活性蛋白C基因突变与儿童间质性肺疾病
- Author:
Xiaole LI
;
Yongsheng XU
- Publication Type:Journal Article
- Keywords:
Children;
Interstitial lung disease;
Surfactant protein C;
Gene mutation
- From:
International Journal of Pediatrics
2016;43(3):193-196
- CountryChina
- Language:Chinese
-
Abstract:
Surfactant protein C(SP-C)is found to be expressed only in the alveolar type Ⅱ cells(AECⅡ),surfactant protein C gene mutations are found to be associated with Children interstitial lung disease.This review discusses the mechanism,diagnosis and therapy of the interstitial lung disease induced by the surfactant protein C gene mutations.
