Moyamoya-Like Vasculopathy in Neurosarcoidosis.
10.3340/jkns.2009.45.1.50
- Author:
Jun Kyeung KO
1
;
Sang Weon LEE
;
Chang Hwa CHOI
Author Information
1. Department of Neurosurgery, School of Medicine, Pusan National University, Busan, Korea. sangweonlee@pusan.ac.kr
- Publication Type:Case Report
- Keywords:
Moyamoya disease;
Neurosarcoidosis;
Hydrocephalus
- MeSH:
Adult;
Angiography, Digital Subtraction;
Biopsy;
Carotid Artery, Internal;
Central Nervous System Diseases;
Erythrocytes;
Granuloma;
Headache;
Humans;
Hydrocephalus;
Magnetic Resonance Angiography;
Magnetic Resonance Imaging;
Memory;
Methylprednisolone;
Moyamoya Disease;
Sarcoidosis;
Septum Pellucidum;
Ventriculoperitoneal Shunt
- From:Journal of Korean Neurosurgical Society
2009;45(1):50-52
- CountryRepublic of Korea
- Language:English
-
Abstract:
A 31-year-old man presented with dull headache and memory disturbance lasting for one week. Computed tomographic scans revealed acute hydrocephalus. The cerebrospinal fluid contained 53 leukocytes/mm3, with a mononuclear preponderance and no erythrocytes. Magnetic resonance imaging revealed hydrocephalus and leptomeningeal enhancement. Magnetic resonance angiography and digital subtraction angiography showed supraclinoid occlusion of the right internal carotid artery, which resembled unilateral moyamoya disease. Neuroendoscopic biopsy of a lesion in the septum pellucidum revealed noncaseating granulomas, which was consistent with sarcoidosis. The patient was successfully managed with intravenous methylprednisolone and ventriculoperitoneal shunting. To our knowledge, this is the first case of moyamoya-like vasculopathy associated with neurosarcoidosis.
