A Case of Intraductal Papillary Mucinous Neoplasm of the Pancreas with Pancreatoduodenal Fistula Diagnosed by Pancreatoscopy Using a Standard Upper Endoscope.
10.15279/kpba.2014.19.1.47
- Author:
Chung Jo CHOI
1
;
Sung Hoon MOON
;
Ja Kyung KIM
;
Bum Joon KIM
;
Ji Won PARK
;
Ho Suk KANG
;
Jong Hyeok KIM
;
Choong Kee PARK
Author Information
1. Departments of Internal Medicine, Hallym University Sacred Heart Hospital, Hallym University College of Medicine, Anyang, Korea. endomoon@naver.com
- Publication Type:Case Report
- Keywords:
Intraductal papillary mucinous neoplasm;
Pancreatoduodenal fistula;
Pancreatoscopy;
Endoscopy
- MeSH:
Adenocarcinoma;
Diagnosis;
Dilatation;
Endoscopes*;
Endoscopy;
Fistula*;
Humans;
Jaundice;
Middle Aged;
Mucins*;
Pancreas*;
Pancreatectomy;
Pancreatic Ducts;
Tomography, X-Ray Computed;
Weight Loss
- From:Korean Journal of Pancreas and Biliary Tract
2014;19(1):47-51
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Intraductal papillary mucinous neoplasm of the pancreas (IPMN) is characterized by the production of mucin and marked dilatation of pancreatic duct. There are only several cases reports about fistula formation with adjacent organs in IPMN. A 61-year-old man was admitted due to jaundice and weight loss. CT scans showed that multiloculated cystic mass had replaced the body and tail of the pancreas. Interestingly, a fistula was found between cystic mass and duodenal bulb. With a diagnosis of malignant IPMN and pancreatoduodenal fistula, endoscopic forcep-biopsy was performed at the orifice of the fistula and pancreatic duct, through the fistula, under a fluoroscopic guidance. Pathologic examination showed only inflammatory cells. Direct peroral pancreatoscopy was performed through the pancreatoduodenal fistula using a standard upper endoscope with saline irrigation. Endoscopic forcep-biopsy was performed on the papillary tumor. Pathologic examination revealed intestinal type IPMN and radical total pancreatectomy was performed. Pathologic examination of the surgical specimen showed tubular adenocarcinoma arising from 15 cm sized intestinal type IPMN.