A Case of Systemic Sclerosis Sine Scleroderma Presenting as Pulmonary Interstitial Fibrosis.
10.4046/trd.2001.50.4.493
- Author:
Jin Ho KWAK
;
Won Il CHOI
;
Seung Hyun LEE
;
Chang Gyun SEO
;
Kyung Chan KIM
;
Min Su KIM
;
Kun Young KWON
;
Soo Ji SUH
;
Chang Kwon PARK
;
Young June JEON
- Publication Type:Case Report
- Keywords:
Systemic sclerosis sine scleroderma;
Pulmonary interstitial fibrosis
- MeSH:
Diagnosis;
Esophageal Sphincter, Lower;
Esophagus;
Fibrosis*;
Humans;
Lung;
Manometry;
Scleroderma, Systemic*;
Sclerosis;
Skin
- From:Tuberculosis and Respiratory Diseases
2001;50(4):493-498
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Lung involvement in systemic sclerosis(SSC) is common but usually occurs late in the course. Skin changes usually occur before the pulmonary findings. In this report, a patient who developed pulmonary interstitial fibrosis without skin changes is presented. A diagnosis of SSC lung involvement was made histologically. The a nti-scl-70 antibody test was positive. Esophageal manometry revealed a lower amplitude in the lower two-third of the esophagus and pressure in the lower esophageal sphincter. Here we report a case of wystemic sclerosis sine scleroderma presenting as pulmonary interstitial fibrosis with a review of the relevant literatures.
