Churg-Strauss Syndrome Presenting with Diffuse Alveolar Hemorrhage.
10.3904/kjm.2015.89.6.738
- Author:
Mi Hee KANG
1
;
Won Seok LEE
;
Yun Jung CHOI
;
Yoo Jeong OH
;
Joo Hee HWANG
;
Wan Hee YOO
Author Information
1. Department of Internal Medicine, Chonbuk National University Medical School and Research Institute of Clinical Medicine of Chonbuk National University Hospital, Jeonju, Korea.
- Publication Type:Case Report
- Keywords:
Churg-Strauss syndrome
- MeSH:
Asthma;
Churg-Strauss Syndrome*;
Diagnosis;
Eosinophilia;
Eosinophils;
Hemorrhage*;
Prognosis;
Systemic Vasculitis;
Vasculitis
- From:Korean Journal of Medicine
2015;89(6):738-741
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Churg-Strauss syndrome (CSS), known as eosinophilic granulomatosis with polyangiitis, is a rare type of systemic vasculitis characterized by the presence of asthma, peripheral eosinophilia, and necrotizing vasculitis with eosinophilic infiltration of multiple organs. Approximately 3-4% of all CSS cases are associated with alveolar hemorrhage. Untreated CSS may lead to a poor prognosis, but glucocorticoid and cytotoxic agent treatments may result in clinical remission. The careful diagnosis and understanding of CSS is important for making treatment decisions and providing effective care. Here, we report a case of CSS with diffuse alveolar hemorrhage.
