A Case of Arrhythmogenic Right Ventricular Dysplasia.
10.4070/kcj.1996.26.6.1204
- Author:
Young Kwon KIM
;
Dong Sun HAN
;
Suk Hoe KWEON
;
Myung In LEE
;
Hak Joong LEE
- Publication Type:Case Report
- Keywords:
Arrhythmogenic right ventricular dysplasia
- MeSH:
Arrhythmias, Cardiac;
Arrhythmogenic Right Ventricular Dysplasia*;
Death, Sudden;
Electrocardiography;
Heart Ventricles;
Myocardium
- From:Korean Circulation Journal
1996;26(6):1204-1209
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Arrhythmogenic right ventricular dysplasia is a rare heart muscle disorder of unknown cause that primarily involves the right ventricle. It is characterized pathologically by fibrofatty replacement of the right ventricular myocardium. Clinical manifestations include structural and functional abnormalities of the right ventricle, electrocardiographic depolarization/repolarization changes, and presentation with sudden death or ventricular arrhythmias of right ventricular origin. It is one of the important causes of the ventricular arrhythmia or sudden death among apparently healthy young people. We report a case of arrhythmogenic right ventricular dysplasia with the review of the literature.